Names & Taxonomy

Uniprot ID:
Q8IUH4
Entry Name:
ZDH13_HUMAN
Status:
reviewed
Protein Names:
Palmitoyltransferase ZDHHC13 (EC 2.3.1.225) (Huntingtin-interacting protein 14-related protein) (HIP14-related protein) (Huntingtin-interacting protein HIP3RP) (Putative MAPK-activating protein PM03) (Putative NF-kappa-B-activating protein 209) (Zinc finger DHHC domain-containing protein 13) (DHHC-13)
Gene Names:
ZDHHC13 HIP14L HIP3RP
Gene Names Primary:
ZDHHC13
Organism:
Homo sapiens (Human)

Structure

Length:
622
Sequence:
MEGPGLGSQCRNHSHGPHPPGFGRYGICAHENKELANAREALPLIEDSSNCDIVKATQYGIFERCKELVEAGYDVRQPDKENVSLLHWAAINNRLDLVKFYISKGAVVDQLGGDLNSTPLHWAIRQGHLPMVILLLQHGADPTLIDGEGFSSIHLAVLFQHMPIIAYLISKGQSVNMTDVNGQTPLMLSAHKVIGPEPTGFLLKFNPSLNVVDKIHQNTPLHWAVAAGNVNAVDKLLEAGSSLDIQNVKGETPLDMALQNKNQLIIHMLKTEAKMRANQKFRLWRWLQKCELFLLLMLSVITMWAIGYILDFNSDSWLLKGCLLVTLFFLTSLFPRFLVGYKNLVYLPTAFLLSSVFWIFMTWFILFFPDLAGAPFYFSFIFSIVAFLYFFYKTWATDPGFTKASEEEKKVNIITLAETGSLDFRTFCTSCLIRKPLRSLHCHVCNCCVARYDQHCLWTGRCIGFGNHHYYIFFLFFLSMVCGWIIYGSFIYLSSHCATTFKEDGLWTYLNQIVACSPWVLYILMLATFHFSWSTFLLLNQLFQIAFLGLTSHERISLQKQSKHMKQTLSLRKTPYNLGFMQNLADFFQCGCFGLVKPCVVDWTSQYTMVFHPAREKVLRSV
Proteomes:
UP000005640

Subcellular location

Subcellular Location:
Golgi apparatus membrane

Function

Function:
Palmitoyltransferase for HD and GAD2. May play a role in Mg(2+) transport.
Catalytic Activity:
Palmitoyl-CoA + -L-cysteine = -S-palmitoyl-L-cysteine + CoA.
Active Site:
ACT_SITE 456 456 S-palmitoyl cysteine intermediate.
Gene Ontology Go:
endoplasmic reticulum
Golgi apparatus
Golgi membrane
Golgi-associated vesicle membrane
integral component of membrane
intracellular membrane-bounded organelle
membrane
magnesium ion transmembrane transporter activity
palmitoyltransferase activity
protein-cysteine S-palmitoyltransferase activity
signal transducer activity
zinc ion binding
positive regulation of I-kappaB kinase/NF-kappaB signaling
signal transduction
Gene Ontology Biological Process:
positive regulation of I-kappaB kinase/NF-kappaB signaling
signal transduction
Gene Ontology Molecular Function:
magnesium ion transmembrane transporter activity
palmitoyltransferase activity
protein-cysteine S-palmitoyltransferase activity
signal transducer activity
zinc ion binding
Gene Ontology Cellular Component:
endoplasmic reticulum
Golgi apparatus
Golgi-associated vesicle membrane
Golgi membrane
integral component of membrane
intracellular membrane-bounded organelle
membrane
Keywords:
ANK repeat
Acetylation
Acyltransferase
Alternative splicing
Complete proteome
Cytoplasmic vesicle
Golgi apparatus
Lipoprotein
Membrane
Metal-binding
Palmitate
Polymorphism
Reference proteome
Repeat
Transferase
Transmembrane
Transmembrane helix
Zinc
Zinc-finger

Publication

PubMed ID:
12393793 12761501 14702039 16554811 15489334 22814378